| Adult MDA5 Dermatomyositis N = 13 | Pediatric MDA5 Dermatomyositis N = 9 | P value |
---|---|---|---|
Mean age at disease onset Years, (SD) | 44.6 (13.9) | 6.5 (4.9) | Â |
Sex (Male, Female) | 5,8 | 3,6 | ns |
Race/Ethnicity | Â | Â | Â |
    Caucasian | 1 | 0 |  |
    Hispanic | 4 | 6 | 0.50 |
    African American | 7 | 3 |  |
    Black Hispanic | 1 | 0 |  |
ILD | Â | Â | Â |
    Absent | 3 | 4 |  |
    Stable ILD | 7 | 4 | 0.61 |
    RP-ILD | 3 | 1 |  |
Skin ulcers | 7 | 6 | 0.67 |
Arthritis | 9 | 7 | ns |
Myositis | 4 | 9 | 0.002 |
Raynaud’s phenomenon | 8 | 3 | 0.39 |
ANA | 6 | 4 | ns |
Ro 52 | 8 | 3 | 0.39 |