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Table 1 Study patient characteristics

From: Antimelanoma differentiation-associated gene 5 (anti-MDA5) antibody-positive dermatomyositis: clinical features and outcomes in a racially diverse patient cohort

 

Adult MDA5 Dermatomyositis

N = 13

Pediatric MDA5 Dermatomyositis

N = 9

P value

Mean age at disease onset Years, (SD)

44.6 (13.9)

6.5 (4.9)

 

Sex (Male, Female)

5,8

3,6

ns

Race/Ethnicity

   

      Caucasian

1

0

 

      Hispanic

4

6

0.50

      African American

7

3

 

      Black Hispanic

1

0

 

ILD

   

      Absent

3

4

 

      Stable ILD

7

4

0.61

      RP-ILD

3

1

 

Skin ulcers

7

6

0.67

Arthritis

9

7

ns

Myositis

4

9

0.002

Raynaud’s phenomenon

8

3

0.39

ANA

6

4

ns

Ro 52

8

3

0.39