Table 4 Imaging, biopsy, and other clinical findings
Variable | N | Overall (N = 19) |
|---|---|---|
MRI positive findings | 2 | 2 (100%) |
Muscle biopsy findings | ||
Polymoysitis | 19 | 0 (0%) |
DM | 19 | 1 (5%) |
MHC | 19 | 0 (0%) |
Complements deposition | 19 | 0 (0%) |
Myopathic features | 19 | 2 (11%) |
Others | 19 | 0 (0%) |
Skin biopsy findings | ||
Interface dermatitis | 19 | 12 (63%) |
Perivascular infiltrate | 19 | 4 (21%) |
Mucin deposition | 19 | 8 (42%) |
Normal | 19 | 1 (5%) |
PFT | ||
FVC | 10 | 3.1 (2.3, 3.6) |
FVC% | 10 | 90.0 (86.0, 97.5) |
DLCO | 10 | 15.3 (13.8, 18.7) |
DLCO% | 10 | 83.5 (71.5, 88.0) |
SPO2 at rest | 10 | 98.0 (97.0, 98.0) |
SPO2 at exertion | 10 | 96.0 (95.2, 96.0) |
EMG findings | ||
Fibrillation potential w/irritative insertional activity | 19 | 5 (26%) |
High frequency repetitive discharges | 19 | 1 (5%) |
Polyphasic potentials of short duration and low amplitude | 19 | 4 (21%) |
Neuropathy | 19 | 0 (0%) |
Non-diagnostic | 19 | 5 (26%) |
Chest findings | ||
NSIP | 19 | 2 (11%) |
UIP | 19 | 0 (0%) |
LIP | 19 | 0 (0%) |
DIP | 19 | 0 (0%) |
DAD | 19 | 0 (0%) |
NSIP w/ OP overlap | 19 | 0 (0%) |
Normal | 19 | 7 (37%) |
Other | 19 | 3 (16%) |